1/6/2024 0 Comments Aren0321 qarcOutcomes of patients with revised stage I clear cell sarcoma of kidney treated in National Wilms Tumor Studies 1-5. Kalapurakal JA, Perlman EJ, Seibel NL, Ritchey M, Dome JS, Grundy PE. Clear cell sarcoma of the kidney in a 62-year-old patient presenting with generalized pruritus. Pediatric and adult primary sarcomas of the kidney: a cross-sectional imaging review. Lalwani N, Prasad SR, Vikram R, Katabathina V, Shanbhogue A, Restrepo C. Clear cell sarcoma of the kidney in children: experience in a developing country. TCF21 hypermethylation in genetically quiescent clear cell sarcoma of the kidney. Gooskens SL, Gadd S, Guidry Auvil JM, Gerhard DS, Khan J, Patidar R, et al. Dysregulated mitogen-activated protein kinase signalling as an oncogenic basis for clear cell sarcoma of the kidney. Kenny C, McDonagh N, Lazaro A, O'Meara E, Klinger R, O'Connor D, et al. Characterization of the chromosomal translocation t(10 17)(q22 p13) in clear cell sarcoma of kidney. O'Meara E, Stack D, Lee CH, Garvin AJ, Morris T, Argani P, et al. Recurrent internal tandem duplications of BCOR in clear cell sarcoma of the kidney. Roy A, Kumar V, Zorman B, Fang E, Haines KM, Doddapaneni H, et al. Whole transcriptome sequencing identifies BCOR internal tandem duplication as a common feature of clear cell sarcoma of the kidney. 55 (2):120-3.Īstolfi A, Melchionda F, Perotti D, Fois M, Indio V, Urbini M, et al. BCOR internal tandem duplication and YWHAE-NUTM2B/E fusion are mutually exclusive events in clear cell sarcoma of the kidney. ![]() Consistent in-frame internal tandem duplications of BCOR characterize clear cell sarcoma of the kidney. Ueno-Yokohata H, Okita H, Nakasato K, Akimoto S, Hata J, Koshinaga T, et al. Late recurrence of clear cell sarcoma of the kidney. Kusumakumary P, Chellam VG, Rojymon J, Hariharan S, Krishnan NM. Delayed Metastasis of Clear Cell Sarcoma of Kidney to Bladder After 7 Disease-Free Years. Bilateral clear cell sarcoma of the kidney. Zekri W, Yehia D, Elshafie MM, Zaghloul MS, El-Kinaai N, Taha H, et al. Manchanda V, Mohta A, Khurana N, Gupta CR, Neogi S. ![]() Outcome of clear cell sarcoma of the kidney (CCSK) treated on the National Wilms Tumor Study-5 (NWTS). Clear cell sarcoma of the kidney: a review of 351 cases from the National Wilms Tumor Study Group Pathology Center. Bone metastasizing renal tumor of childhood: morphological and clinical features, and differences from Wilms' tumor. Undifferentiated sarcoma of the kidney: a tumor of childhood with histopathologic and clinical characteristics distinct from Wilms' tumor. Histopathology and prognosis of Wilms tumors: results from the First National Wilms' Tumor Study. this treatment consists of a radical nephrectomy followed by radiotherapy and chemotherapy with cyclophosphamide, etoposide, vincristine, and doxorubicin for 24 weeks.īeckwith JB, Palmer NF. In the NWTS-5 protocol, patients with all stages of CCSK are treated with the same regimen used in patients who have Wilms tumor with diffuse anaplasia (excluding stage I) The 8-year relapse-free survival rate for localized clear cell sarcoma of the kidney stages I-III is 88%, but late relapses have been known to occur. The overall survival has improved for patients with clear cell sarcoma of the kidney from NWTS-3 to NWTS-4 (83% vs 66.9% at 8 y). ![]() NWTS-4 showed that patients treated with vincristine, doxorubicin, and dactinomycin for 15 months had an improved relapse-free survival rate compared with patients treated for 6 months (87.5% vs 60.6% at 8 y). In the third National Wilms Tumor Study (NWTS-3), the addition of doxorubicin to the combination of vincristine, dactinomycin, and radiation therapy resulted in an improvement in disease-free survival in patients with clear cell sarcoma of the kidney. The approach for treating clear cell sarcoma of the kidney (CCSK) is different from the approach for Wilms tumor because the overall survival of children with clear cell sarcoma of the kidney remains considerably lower than that of patients with favorable-histology Wilms tumor.
0 Comments
Leave a Reply. |
AuthorWrite something about yourself. No need to be fancy, just an overview. ArchivesCategories |